Christopher A. Ross
Active 1981–2025
- 243
- Papers
- 56,760
- Citations
- 132
- h-index
- 240
- i10-index
Citations
Citation sources
Countries
Institutions
- Johns Hopkins University1.7%
- Johns Hopkins Medicine1.3%
- Harvard University1.1%
- University College London1%
- Massachusetts General Hospital0.8%
- Inserm0.8%
- Other93.3%
Fields
- Neuroscience37.7%
- Medicine29%
- Biochemistry, Genetics and Molecular Biology28.8%
- Immunology and Microbiology0.8%
- Psychology0.7%
- Computer Science0.5%
- Other2.5%
Topics
- Genetic Neurodegenerative Diseases10.1%
- Mitochondrial Function and Pathology6.5%
- Parkinson's Disease Mechanisms and Treatments5.1%
- Alzheimer's disease research and treatments3.4%
- Neurological disorders and treatments3.2%
- Neuroscience and Neuropharmacology Research2.5%
- Other69.2%
Coauthors
- Russell L. Margolis57
- Michael R. Hayden25
- Adam Rosenblatt21
- Alan H. Sharp20
- Wenzhen Duan19
- Akira Sawa18
- Jane S. Paulsen18
- Nicolas Arbez18
- Elizabeth Aylward17
- Wanli W. Smith17
- Solomon H. Snyder16
- Ted M. Dawson16
- Frederick C. Nucifora14
- Juan C. Troncoso14
- Gabriele Schilling13
- Susumu Mori13
- Martha Nance12
- Peng Qi12
- Valina L. Dawson12
- David Borchelt11
- Douglas R. Langbehn11
- Jason Brandt11
- Mali Jiang11
- Tamara Ratovitski11
All papers
- Huntington disease
Authors: Gillian P. Bates, Ray Dorsey, James F. Gusella, Michael R. Hayden, Chris Kay, Blair R. Leavitt, Martha Nance, Christopher A. Ross, Rachael I. Scahill, Ronald Wetzel, Edward J. Wild, Sarah J. Tabrizi - Nature Reviews Disease Primers 2015 cited by 1,577
- Protein aggregation and neurodegenerative disease
Authors: Christopher A. Ross, Michelle A. Poirier - Nature Medicine 2004 cited by 3,467
- Huntington disease: new insights into molecular pathogenesis and therapeutic opportunities
Authors: Sarah J. Tabrizi, Michael Flower, Christopher A. Ross, Edward J. Wild - Nature Reviews Neurology 2020 cited by 532
- Huntington's disease: from molecular pathogenesis to clinical treatment
Authors: Christopher A. Ross, Sarah J. Tabrizi - The Lancet Neurology 2010 cited by 1,726
- A biological classification of Huntington's disease: the Integrated Staging System
Authors: Sarah J. Tabrizi, Scott Schobel, Emily C. Gantman, Alexandra Mansbach, Beth Borowsky, Pavlina Konstantinova, Tiago Mestre, Jennifer Panagoulias, Christopher A. Ross, Maurice Zauderer, Ariana P. Mullin, Klaus Romero, Sudhir Sivakumaran, Emily C. Turner, Jeffrey D. Long, Cristina Sampaio - The Lancet Neurology 2022 cited by 301
- Huntington disease: natural history, biomarkers and prospects for therapeutics
Authors: Christopher A. Ross, Elizabeth Aylward, Edward J. Wild, Douglas R. Langbehn, Jeffrey D. Long, John Harley Warner, Rachael I. Scahill, Blair R. Leavitt, Julie C. Stout, Jane S. Paulsen, Ralf Reilmann, Paul G. Unschuld, Alice Wexler, Russell L. Margolis, Sarah J. Tabrizi - Nature Reviews Neurology 2014 cited by 1,009
- Parkinson's disease-associated mutations in leucine-rich repeat kinase 2 augment kinase activity
Authors: Andrew B. West, Darren J. Moore, Saskia Biskup, Artem Bugayenko, Wanli W. Smith, Christopher A. Ross, Valina L. Dawson, Ted M. Dawson - National Academy of Sciences, Proceedings of the National Academy of Sciences 2005 cited by 1,238
- Mutant Huntingtin Disrupts the Nuclear Pore Complex
Authors: Jonathan C. Grima, J. Gavin Daigle, Nicolas Arbez, Kathleen M. Cunningham, Ke Zhang, Joseph Ochaba, Charlene Geater, Eva L. Morozko, Jennifer Stocksdale, Jenna Glatzer, Jacqueline T. Pham, Ishrat Ahmed, Peng Qi, Harsh Wadhwa, Olga Pletniková, Juan C. Troncoso, Wenzhen Duan, Solomon H. Snyder, Laura P.W. Ranum, Leslie M. Thompson, Thomas E. Lloyd, Christopher A. Ross, Jeffrey D. Rothstein - Neuron 2017 cited by 371
- Preventing amyotrophic lateral sclerosis: insights from pre-symptomatic neurodegenerative diseases
Authors: Michael Benatar, Joanne Wuu, Caroline McHutchison, Ronald B. Postuma, Bradley F. Boeve, Ronald C. Petersen, Christopher A. Ross, Howard J. Rosen, Jalayne J. Arias, Stephanie Fradette, Michael McDermott, Jeremy M. Shefner, Christine Stanislaw, Sharon Abrahams, Stephanie Cosentino, Peter M Andersen, Richard S. Finkel, Volkan Granit, Anne‐Laure Grignon, Jonathan D. Rohrer, Corey T. McMillan, Murray Grossman, Ammar Al-Chalabi, Martin R. Turner, First International Pre-Symptomatic ALS Workshop, Ammar Al-Chalabi, Peter M Andersen, Jalayne J. Arias, Michael Benatar, Bradley F. Boeve, Stephanie Cosentino, Kuldip D. Dave, Toby A. Ferguson, Mary-Kay Floeter, Jonathan D. Rohrer, Stephanie Fradette, Tania F. Gendron, Volkan Granit, Anne‐Laure Grignon, Murray Grossman, Amelie K. Gubitz, Petra Kaufman, Isabelle Le Ber, Suzee Lee, Andrea Malaspina, Michael McDermott, Caroline McHutchison, Corey T. McMillan, Katie Nicholson, Ronald C. Petersen, Ronald B. Postuma, Richard Robinson, Howard J. Rosen, Christopher A. Ross, Jeremy M. Shefner, Christine Stanislaw, Nadine Tatton, Neil Thakur, Martin R. Turner, Jochen H. Weishaupt, Joanne Wuu - Brain 2021 cited by 116
- Formation of Neuronal Intranuclear Inclusions Underlies the Neurological Dysfunction in Mice Transgenic for the HD Mutation
Authors: Stephen W. Davies, Mark Turmaine, Barbara A. Cozens, Marian DiFiglia, Alan H. Sharp, Christopher A. Ross, Eberhard Scherzinger, Erich E. Wanker, Laura Mangiarini, Gillian P. Bates - Cell 1997 cited by 2,203
- Trinucleotide repeat length instability and age of onset in Huntington's disease
Authors: Mabel P. Duyao, C M Ambrose, Richard H. Myers, Andrea Novelletto, Francesca Persichetti, Marina Frontali, Susan E. Folstein, Christopher A. Ross, Mary L. Franz, M Abbott, J. Gray, P.M. Conneally, A. B. Young, John B. Penney, Zane Hollingsworth, Ira Shoulson, Alice Lazzarini, Arthur Falek, Walter J. Koroshetz, Daniel S. Sax, Edward J. Bird, Jean Paul Vonsattel, E. Bonilla, José Alvir, Jaime Conde, Jeong‐Heon Cha, Leon Dure, F. Gomez, María Ramos, Juan Sanchez‐Ramos, S. Robert Snodgrass, Margot de Young, Nancy S. Wexler, Chaya Moscowitz, Graciela K. Penchaszadeh, H MacFarlane, Mark J. Anderson, Bruce G. Jenkins, Jayalakshmi Srinidhi, Glenn Barnes, James F. Gusella, Marcy E. MacDonald - Nature Genetics 1993 cited by 1,099
- Synaptic dysregulation in a human iPS cell model of mental disorders
Authors: Zhexing Wen, Ha Nam Nguyen, Ziyuan Guo, Matthew A. Lalli, Xinyuan Wang, Yijing Su, Nam-Shik Kim, Ki‐Jun Yoon, Jaehoon Shin, Ce Zhang, Georgia Makri, David W. Nauen, Huimei Yu, Elmer Guzman, Cheng-Hsuan Chiang, Nadine Yoritomo, Kozo Kaibuchi, Jizhong Zou, Kimberly M. Christian, Linzhao Cheng, Christopher A. Ross, Russell L. Margolis, Gong Chen, Kenneth S. Kosik, Hongjun Song, Guo‐li Ming - Nature 2014 cited by 568
- CAG repeat expansion in Huntington disease determines age at onset in a fully dominant fashion
Authors: J.-M. Lee, E.M. Ramos, J.-H. Lee, Tammy Gillis, Jayalakshmi Srinidhi Mysore, Michael R. Hayden, Simon C. Warby, PJ Morrison, Martha Nance, Christopher A. Ross, Russell L. Margolis, Ferdinando Squitieri, S. Orobello, Stefano Di Donato, Estrella Gómez‐Tortosa, Carmen Ayuso, Oksana Suchowersky, R J Trent, Elizabeth McCusker, Andrea Novelletto, Marina Frontali, Randi Jones, Tetsuo Ashizawa, Samuel Frank, Marie Saint‐Hilaire, Steven M. Hersch, H. Diana Rosas, Diane Lucente, Madeline Harrison, Andrea Zanko, Ruth K. Abramson, Karen Marder, Jorge Sequeiros, Jane S. Paulsen, G. Bernhard Landwehrmeyer, Richard H. Myers, Marcy E. MacDonald, James F. Gusella, Alexandra Dürr, Adam Rosenblatt, Luigi Frati, Susan B. Perlman, P. M. Conneally, Mary Lou Klimek, Melissa Diggin, Tiffany C. Hadzi, Ayana Duckett, Anwar Ahmed, Paul Allen, David Ames, Christine Anderson, Karla J. Anderson, Karen Anderson, Thomasin Andrews, John Ashburner, Eric Axelson, Elizabeth Aylward, Roger A. Barker, Katrin Barth, Stacey K. Barton, Kathleen Baynes, Alexandra Bea, Erik B. Beall, Mirza Faisal Beg, Leigh J. Beglinger, Kevin Biglan, K. Björk, Steve Blanchard, Jeremy Bockholt, Sudharshan Reddy Bommu, Bradley G. Brossman, Maggie Burrows, Vince D. Calhoun, Noelle E. Carlozzi, Amy M. Chesire, Edmond Chiu, Phyllis Chua, R.J. Connell, Carmela Connor, Jody Corey‐Bloom, David Craufurd, Stephen Cross, Lucette A. Cysique, Rachelle Dar Santos, Jennifer Davis, Joji Decolongon, A. Dipietro, Nicholas Doucette, Nancy R. Downing, Ann Dudler, Steve Dunn, Daniel Ecker, Eric A. Epping, Diane Erickson, Cheryl Erwin, Kenneth Evans, Stewart A. Factor, Sarah Tomaszewski Farias, Marta Fatas, Jess G. Fiedorowicz and 611 more - Neurology 2012 cited by 391
- Neuroprotective role of Sirt1 in mammalian models of Huntington's disease through activation of multiple Sirt1 targets
Authors: Mali Jiang, Jiawei Wang, Jinrong Fu, Lin Du, Hyunkyung Jeong, Tim West, Lan Xiang, Peng Qi, Zhipeng Hou, Huan Cai, Tamara Seredenina, Nicolas Arbez, Shanshan Zhu, Katherine Sommers, Jennifer Qian, Jiangyang Zhang, Susumu Mori, X. William Yang, Kellie L. Tamashiro, Susan Aja, Timothy H. Moran, Ruth Luthi‐Carter, Bronwen Martin, Stuart Maudsley, Mark P. Mattson, Robert H. Cichewicz, Christopher A. Ross, David M. Holtzman, Dimitri Krainc, Wenzhen Duan - Nature Medicine 2011 cited by 344
- Abnormal degradation of the neuronal stress-protective transcription factor HSF1 in Huntington’s disease
Authors: Rocío Gómez‐Pastor, Eileen T. Burchfiel, Daniel W. Neef, Alex M. Jaeger, Elisa Cabiscol, Spencer U. McKinstry, Argenia L.N. Doss, Alejandro Aballay, Donald C. Lo, Sergey Akimov, Christopher A. Ross, Çağla Eroğlu, Dennis J. Thiele - Nature Communications 2017 cited by 229
- Parkin Mediates Nonclassical, Proteasomal-Independent Ubiquitination of Synphilin-1: Implications for Lewy Body Formation
Authors: Kah Leong Lim, Katherine C. M. Chew, Jeanne M.M. Tan, Cheng Wang, Kenny K. K. Chung, Yi Zhang, Yuji Tanaka, Wanli W. Smith, Simone Engelender, Christopher A. Ross, Valina L. Dawson, Ted M. Dawson - Journal of Neuroscience 2005 cited by 556
- RAN Translation in Huntington Disease
Authors: Mónica Báñez-Coronel, Fatma Ayhan, Alex D. Tarabochia, Tao Zu, B. Pérez, Solaleh Khoramian Tusi, Olga Pletniková, David Borchelt, Christopher A. Ross, Russell L. Margolis, Anthony T. Yachnis, Juan C. Troncoso, Laura P.W. Ranum - Neuron 2015 cited by 352
- trans-(−)-ε-Viniferin Increases Mitochondrial Sirtuin 3 (SIRT3), Activates AMP-activated Protein Kinase (AMPK), and Protects Cells in Models of Huntington Disease
Authors: Jinrong Fu, Jing Jin, Robert H. Cichewicz, Serena A. Hageman, Trevor K. Ellis, Lan Xiang, Peng Qi, Mali Jiang, Nicolas Arbez, Katelyn Hotaling, Christopher A. Ross, Wenzhen Duan - Journal of Biological Chemistry 2012 cited by 209
- What is the role of protein aggregation in neurodegeneration?
Authors: Christopher A. Ross, Michelle A. Poirier - Nature Reviews Molecular Cell Biology 2005 cited by 604
- Acute Kidney Injury Leads to Inflammation and Functional Changes in the Brain
Authors: Manchang Liu, Yideng Liang, Srinivasulu Chigurupati, Justin D. Lathia, Mikhail V. Pletnikov, Zhaoli Sun, Michael T. Crow, Christopher A. Ross, Mark P. Mattson, Hamid Rabb - Journal of the American Society of Nephrology 2008 cited by 396
- Safety and efficacy of pridopidine in patients with Huntington's disease (PRIDE-HD): a phase 2, randomised, placebo-controlled, multicentre, dose-ranging study
Authors: Ralf Reilmann, Andrew McGarry, Igor D. Grachev, Juha‐Matti Savola, Beth Borowsky, Eli Eyal, Nicholas J. Gross, Douglas R. Langbehn, Robin Schubert, Anna Teige Wickenberg, Spyros Papapetropoulos, Michael R. Hayden, Ferdinando Squitieri, Karl Kieburtz, G. Bernhard Landwehrmeyer, Pinky Agarwal, Karen E. Anderson, Nasir A Aziz, J.P. Azulay, Anne‐Catherine Bachoud‐Lévi, Roger A. Barker, Agnieszka Bebak, Markus Beuth, Kevin Biglan, Stéphanie Blin, Stefan Bohlen, Raphael M. Bonelli, Sue Caldwell, Fabienne Calvas, Jonielyn Carlos, Simona Castagliuolo, Terrence Chong, Phyllis Chua, Allison Coleman, Jody Corey‐Bloom, Rebecca Cousins, David Craufurd, Jill Davison, E Decorte, Giuseppe De Michele, Laura Dornhege, Andrew Feigin, Stephanie Gallehawk, Pascale Gauteul, Carey Gonzales, Jane Griffith, А.В. Густов, Mark Guttman, Beatrix Heim, Hope Heller, Lena E. Hjermind, С. Н. Иллариошкин, Larry Ivanko, Jessica Jaynes, Mollie W. Jenckes, Barbara J. Kaminski, Anne Kampstra, Agnieszka Konkel, S V Kopishinskaya, Pierre Krystkowiak, Suresh K Komati, Alexander Kwako, Stefan Lakoning, Guzal Latipova, Blair R. Leavitt, Clement T. Loy, Cheryl MacFarlane, Louise Madsen, Karen Marder, Sarah Mason, Neila Mendis, Tilak Mendis, Andrea H. Németh, Louise Nevitt, Virginia Norris, Christine J. O’Neill, Audrey Olivier, Michael Orth, Ashley Owens, Peter K. Panegyres, Susan Perlman, J. Samuel Preston, Josef Priller, Alicja Puch, Oliver Quarrell, Domenica Ragosta, Amandine Rialland, Hugh Rickards, Anna Maria Romoli, Christopher A. Ross, Anne Rosser, Monika Rudzińska, Cinzina V Russo, Carsten Saft, Victoria Segro, Klaus Seppi, Barbara Shannon, David Shprecher, C. Simonin, Zara Skitt and 20 more - The Lancet Neurology 2018 cited by 108
- Interference by Huntingtin and Atrophin-1 with CBP-Mediated Transcription Leading to Cellular Toxicity
Authors: Frederick C. Nucifora, Masayuki Sasaki, Matthew F. Peters, Hui Huang, Jillian K. Cooper, Mitsunori Yamada, Hitoshi Takahashi, Shoji Tsuji, Juan C. Troncoso, Valina L. Dawson, Ted M. Dawson, Christopher A. Ross - Science 2001 cited by 1,094
- Quantitative Susceptibility Mapping Suggests Altered Brain Iron in Premanifest Huntington Disease
Authors: Jiri M.G. Van Bergen, Jun Hua, Paul G. Unschuld, Issel Anne L. Lim, Craig Jones, Russell L. Margolis, Christopher A. Ross, Peter C.M. van Zijl, Xu Li - American Journal of Neuroradiology 2015 cited by 149
- Neuroprotective effects of PPAR‐γ agonist rosiglitazone in N171‐82Q mouse model of Huntington's disease
Authors: Jing Jin, Jennifer Albertz, Zhihong Guo, Peng Qi, Gay Rudow, Juan C. Troncoso, Christopher A. Ross, Wenzhen Duan - Journal of Neurochemistry 2013 cited by 120
