Françoise Le Deist
Active 1986–2016
- Also published as
- Françoise le Deist
- 99
- Papers
- 32,835
- Citations
- 89
- h-index
- 99
- i10-index
Citations
Citation sources
Countries
Institutions
Fields
- Biochemistry, Genetics and Molecular Biology38.9%
- Medicine31.9%
- Immunology and Microbiology25.3%
- Neuroscience2%
- Engineering0.5%
- Agricultural and Biological Sciences0.4%
- Other1%
Topics
- Immune Cell Function and Interaction6.9%
- Virus-based gene therapy research5.4%
- Immunodeficiency and Autoimmune Disorders5.2%
- T-cell and B-cell Immunology4%
- CRISPR and Genetic Engineering3.8%
- RNA Interference and Gene Delivery3.5%
- Other71.2%
Coauthors
- Alain Fischer81
- Geneviève de Saint Basile34
- Marina Cavazzana30
- Stéphane Blanche29
- Jean‐Laurent Casanova16
- Jean‐Pierre de Villartay16
- C Griscelli12
- Frédéric Rieux‐Laucat11
- Élie Haddad11
- Anne Durandy10
- Malika Benkerrou10
- Claire Hivroz8
- Nicole Brousse8
- Capucine Pïcard7
- Despina Moshous7
- E Vilmer7
- Salima Hacein‐Bey‐Abina7
- Sophie Dupuis‐Girod7
- Nada Jabado6
- Stéphanie Certain6
- Christine Bodemer5
- Marianne Debré5
- Nadine Cerf–Bensussan5
- Régina de Chasseval5
All papers
- LMO2 -Associated Clonal T Cell Proliferation in Two Patients after Gene Therapy for SCID-X1
Authors: S. Hacein-Bey-Abina, Christof von Kalle, Manfred Schmidt, Matthew P. McCormack, N. M. Wulffraat, Philippe Leboulch, Apiradee Lim, Cameron S. Osborne, Robert Pawliuk, Estelle Morillon, Ricardo U. Sorensen, A. Förster, Peter Fraser, J. I. Cohen, Geneviève de Saint Basile, Ian E. Alexander, Uwe Wintergerst, Thierry Frébourg, Alain Aurias, Dominique Stoppa‐Lyonnet, Serge Romana, I Radford-Weiss, Fabian Gross, F Valensi, Éric Delabesse, Elizabeth Macintyre, F Sigaux, Jean Soulier, Lily E. Leiva, Manuela Wissler, Claudia Prinz, Terence H. Rabbitts, Françoise Le Deist, Alain Fischer, Marina Cavazzana - Science 2003 cited by 3,561
- A Serious Adverse Event after Successful Gene Therapy for X-Linked Severe Combined Immunodeficiency
Authors: Salima Hacein‐Bey‐Abina, Christof von Kalle, Manfred Schmidt, Françoise Le Deist, N. M. Wulffraat, Elisabeth McIntyre, Isabelle Radford, Jean‐Luc Villeval, Christopher C. Fraser, Marina Cavazzana, Alain Fischer - New England Journal of Medicine 2003 cited by 1,847
- Perforin Gene Defects in Familial Hemophagocytic Lymphohistiocytosis
Authors: Susan E. Stepp, Rémi Dufourcq-Lagelouse, Françoise Le Deist, Sadhna Bhawan, Stéphanie Certain, Porunelloor A. Mathew, Jan‐Inge Henter, Michael Bennett, Alain Fischer, Geneviève de Saint Basile, Vinay Kumar - Science 1999 cited by 1,235
- Gene Therapy of Human Severe Combined Immunodeficiency (SCID)-X1 Disease
Authors: Marina Cavazzana, Salima Hacein‐Bey, Geneviève de Saint Basile, Fabian Gross, Éric Yvon, Patrick Nusbaum, Françoise Selz, Christophe Hue, Stéphanie Certain, Jean‐Laurent Casanova, Philippe Bousso, Françoise Le Deist, Alain Fischer - Science 2000 cited by 2,627
- Mutations in Fas Associated with Human Lymphoproliferative Syndrome and Autoimmunity
Authors: Frédéric Rieux‐Laucat, Françoise Le Deist, Claire Hivroz, Irene Roberts, Klaus‐Michael Debatin, Alain Fischer, Jean‐Pierre de Villartay - Science 1995 cited by 1,299
- Autoimmune Lymphoproliferative Syndrome with SomaticFasMutations
Authors: Eliska Hölzelova, Cédric Vonarbourg, Marie‐Claude Stolzenberg, Peter D. Arkwright, Françoise Selz, Anne‐Marie Prieur, Stéphane Blanche, Jiřina Bartůňková, E Vilmer, Alain Fischer, Françoise Le Deist, Frédéric Rieux‐Laucat - New England Journal of Medicine 2004 cited by 327
- Mutations in RAB27A cause Griscelli syndrome associated with haemophagocytic syndrome
Authors: Gaël Ménasché, Élodie Pastural, Jérôme Feldmann, Stéphanie Certain, Fügen Ersoy, Sophie Dupuis, Nico Wulffraat, Diana W. Bianchi, Alain Fischer, Françoise Le Deist, Geneviève de Saint Basile - Nature Genetics 2000 cited by 952
- Munc13-4 Is Essential for Cytolytic Granules Fusion and Is Mutated in a Form of Familial Hemophagocytic Lymphohistiocytosis (FHL3)
Authors: Jérôme Feldmann, Isabelle Callebaut, Graça Raposo, Stéphanie Certain, Delphine Bacq, Cécile Dumont, Nathalie Lambert, O Marie, Gaëlle Chédeville, Hannah Tamary, Véronique Minard‐Colin, E Vilmer, Stéphane Blanche, Françoise Le Deist, Alain Fischer, Geneviève de Saint Basile - Cell 2003 cited by 939
- XIAP deficiency in humans causes an X-linked lymphoproliferative syndrome
Authors: Stéphanie Rigaud, Marie‐Claude Fondanèche, Nathalie Lambert, Benoit Pasquier, Véronique Mateo, Pauline Soulas‐Sprauel, Lionel Galicier, Françoise Le Deist, Frédéric Rieux‐Laucat, Patrick Revy, Alain Fischer, Geneviève de Saint Basile, Sylvain Latour - Nature 2006 cited by 705
- Human mesenchymal stromal cell-secreted lactate induces M2-macrophage differentiation by metabolic reprogramming
Authors: Silvia Selleri, Panojot Bifsha, Sara Civini, Consiglia Pacelli, Mame Massar Dieng, William Lemieux, Ping Jin, Renée Bazin, Natacha Patey, Francesco M. Marincola, Florina Moldovan, Charlotte Zaouter, Louis‐Éric Trudeau, Basma Benabdhalla, Isabelle Louis, Christian Beauséjour, David F. Stroncek, Françoise Le Deist, Élie Haddad - Oncotarget 2016 cited by 177
- Sustained Correction of X-Linked Severe Combined Immunodeficiency by ex Vivo Gene Therapy
Authors: Salima Hacein‐Bey‐Abina, Françoise Le Deist, Frédérique Carlier, Cécile Bouneaud, Christophe Hue, Jean‐Pierre de Villartay, Adrian J. Thrasher, N. M. Wulffraat, Ricardo Sorensen, Sophie Dupuis‐Girod, Alain Fischer, E. Graham Davies, Wietse Kuis, Lilly Leiva, Marina Cavazzana - New England Journal of Medicine 2002 cited by 1,051
- Clinical similarities and differences of patients with X-linked lymphoproliferative syndrome type 1 (XLP-1/SAP deficiency) versus type 2 (XLP-2/XIAP deficiency)
Authors: Jana Pachlopnik Schmid, Danielle Canioni, Despina Moshous, Fabien Touzot, Nizar Mahlaoui, Fabian Hauck, Hirokazu Kanegane, Eduardo López‐Granados, Ester Mejstříková, Isabelle Pellier, Lionel Galicier, Claire Galambrun, Vincent Barlogis, Pierre Bordigoni, A Fourmaintraux, M. Hamidou, A. Dabadie, Françoise Le Deist, Filomeen Haerynck, O Marie, Pierre‐Simon Rohrlich, Jean‐Louis Stephan, Christelle Lenoir, Stéphanie Rigaud, Nathalie Lambert, Michèle Milili, Claudin Schiff, Helen Chapel, Capucine Pïcard, Geneviève de Saint Basile, Stéphane Blanche, Alain Fischer, Sylvain Latour - Blood 2010 cited by 366
- Impairment of Mycobacterial Immunity in Human Interleukin-12 Receptor Deficiency
Authors: Frédéric Altare, Anne Durandy, David A. Lammas, Jean‐François Emile, Salma Lamhamedi, Françoise Le Deist, Pam Drysdale, Emmanuelle Jouanguy, Rainer Döffinger, Françoise Bernaudin, Olle Jeppsson, Jared Gollob, Edgar Meinl, Anthony W. Segal, Alain Fischer, Dinakantha Kumararatne, Jean‐Laurent Casanova - Science 1998 cited by 844
- Munc18-2 deficiency causes familial hemophagocytic lymphohistiocytosis type 5 and impairs cytotoxic granule exocytosis in patient NK cells
Authors: Marjorie Côte, Mickaël Ménager, Agathe Burgess, Nizar Mahlaoui, Capucine Pïcard, Catherine Schaffner, Fahad AlManjomi, Musa Alharbi, Abdullah Alangari, Françoise Le Deist, Andrew R. Gennery, Nathalie Prince, Astrid Cariou, Patrick Nitschké, Ulrich Blank, Gehad ElGhazali, Gaël Ménasché, Sylvain Latour, Alain Fischer, Geneviève de Saint Basile - Journal of Clinical Investigation 2009 cited by 349
- X-linked anhidrotic ectodermal dysplasia with immunodeficiency is caused by impaired NF-κB signaling
Authors: Rainer Döffinger, Asma Smahi, Christine Bessia, Frédéric Geissmann, Jacqueline Feinberg, Anne Durandy, Christine Bodemer, Sue Kenwrick, Sophie Dupuis‐Girod, Stéphane Blanche, Philip Wood, Smail Hadj Rabia, Denis J. Headon, Paul A. Overbeek, Françoise Le Deist, Steven M. Holland, Kiran Belani, Dinakantha Kumararatne, Alain Fischer, Ralph Shapiro, Mary Ellen Conley, Eric Reimund, Hermann Kalhoff, Mario Abinun, Arnold Münnich, Alain Israël, Gilles Courtois, Jean‐Laurent Casanova - Nature Genetics 2001 cited by 819
- Artemis, a Novel DNA Double-Strand Break Repair/V(D)J Recombination Protein, Is Mutated in Human Severe Combined Immune Deficiency
Authors: Despina Moshous, Isabelle Callebaut, Régina de Chasseval, Barbara Corneo, Marina Cavazzana, Françoise Le Deist, İlhan Tezcan, Özden Sanal, Yves Bertrand, Noël Philippe, Alain Fischer, Jean‐Pierre de Villartay - Cell 2001 cited by 904
- Numbers of T cell receptor (TCR) alpha beta+ but not of TcR gamma delta+ intraepithelial lymphocytes correlate with the grade of villous atrophy in coeliac patients on a long term normal diet.
Authors: Tufan Kutlu, Nicole Brousse, Caroline Rambaud, Françoise Le Deist, J. Schmitz, Nadine Cerf–Bensussan - Gut 1993 cited by 177
- CD40-CD40L independent Ig gene hypermutation suggests a second B cell diversification pathway in humans
Authors: Sandra Weller, Ahmad Faili, Corinne Garcia, Moritz Braun, Françoise Le Deist, Geneviève de Saint Basile, Olivier Hermine, Alain Fischer, Claude–Agnès Reynaud, Jean–Claude Weill - National Academy of Sciences, Proceedings of the National Academy of Sciences 2001 cited by 392
- Anti–B-Cell Monoclonal Antibody Treatment of Severe Posttransplant B-Lymphoproliferative Disorder: Prognostic Factors and Long-Term Outcome
Authors: Malika Benkerrou, Jean‐Philippe Jaïs, Véronique Leblond, Anne Durandy, Laurent Sutton, Pierre Bordigoni, Jane Luce Garnier, J. Le Bidois, Françoise Le Deist, Stéphane Blanche, Alain Fischer - Blood 1998 cited by 256
- Long-term outcome after hematopoietic stem cell transplantation of a single-center cohort of 90 patients with severe combined immunodeficiency
Authors: Bénédicte Neven, Sandrine Leroy, Hélène Decaluwe, Françoise Le Deist, Capucine Pïcard, Despina Moshous, Nizar Mahlaoui, Marianne Debré, Jean‐Laurent Casanova, Liliane Dal Cortivo, Yoann Madec, Salima Hacein‐Bey‐Abina, Geneviève de Saint Basile, Jean‐Pierre de Villartay, Stéphane Blanche, Marina Cavazzana, Alain Fischer - Blood 2009 cited by 245
- Cernunnos, a Novel Nonhomologous End-Joining Factor, Is Mutated in Human Immunodeficiency with Microcephaly
Authors: Dietke Buck, Laurent Malivert, Régina de Chasseval, Arthur Bertin Barraud, Marie‐Claude Fondanèche, Özden Sanal, Alessandro Plebani, Jean‐Louis Stephan, Markus Hufnagel, Françoise Le Deist, Alain Fischer, Anne Durandy, Jean‐Pierre de Villartay, Patrick Revy - Cell 2006 cited by 704
- Anti–B-Cell Monoclonal Antibodies in the Treatment of Severe B-Cell Lymphoproliferative Syndrome Following Bone Marrow and Organ Transplantation
Authors: Alain Fischer, Stéphane Blanche, J. Le Bidois, Pierre Bordigoni, Jane Luce Garnier, Patrick Niaudet, Frédéric Morinet, Françoise Le Deist, Anne‐Marie Fischer, C Griscelli, M. Hirn - New England Journal of Medicine 1991 cited by 354
- Low Penetrance, Broad Resistance, and Favorable Outcome of Interleukin 12 Receptor β1 Deficiency
Authors: Claire Fieschi, Stéphanie Boisson‐Dupuis, Émilie Catherinot, Jacqueline Feinberg, Jacinta Bustamante, Adrien Breiman, Frédéric Altare, Richard Baretto, Françoise Le Deist, Samer Kayal, Hartmut Koch, Darko Richter, Martin Brezina, Güzide Aksu, P. Wood, Suliman Aljumaah, Miquel Raspall‐Chaure, Alberto José da Silva Duarte, David Tuerlinckx, J L Virelizier, Alain Fischer, Andrea M. Enright, Jutta Bernhöft, Aileen M. Cleary, Christiane Vermylen, Carlos Rodríguez‐Gallego, Graham Davies, Renate Blütters‐Sawatzki, Claire-Anne Siegrist, Mohammad Ehlayel, Vas Novelli, W. Haas, Jacob Levy, Joachim Freihorst, Sami Al-Hajjar, David Nadal, Dewton de Moraes Vasconcelos, Olle Jeppsson, Necil Kütükçüler, Klára Frecerová, Isabel Caragol, David A. Lammas, Dinakantha Kumararatne, Laurent Abel, Jean‐Laurent Casanova - The Journal of Experimental Medicine 2003 cited by 303
- Hematopoietic Stem Cell Transplantation in Hemophagocytic Lymphohistiocytosis: A Single-Center Report of 48 Patients
Authors: O Marie, Caroline Elie, Geneviève de Saint Basile, Françoise Le Deist, Nizar Mahlaoui, Capucine Pïcard, Bénédicte Neven, Jean‐Laurent Casanova, Marc Tardieu, Marina Cavazzana, Stéphane Blanche, Alain Fischer - PEDIATRICS 2006 cited by 279
