Massimo Zeviani
1984–2025 年に発表
- 222
- 論文数
- 43,880
- 被引用数
- 116
- h 指数
- 220
- i10 指数
被引用数
引用元
国・地域
機関
分野
- Biochemistry, Genetics and Molecular Biology63.4%
- Medicine27.9%
- Neuroscience4.8%
- Immunology and Microbiology1%
- Environmental Science0.4%
- Agricultural and Biological Sciences0.4%
- その他2.1%
トピック
- Mitochondrial Function and Pathology16.1%
- Metabolism and Genetic Disorders6.8%
- ATP Synthase and ATPases Research6.2%
- RNA modifications and cancer4.4%
- Neurogenetic and Muscular Disorders Research4.1%
- Adipose Tissue and Metabolism2%
- その他60.4%
共著者
- Valeria Tiranti41
- Carlo Viscomi35
- Erika Fernández‐Vizarra33
- Eleonora Lamantea30
- Daniele Ghezzi29
- Costanza Lamperti28
- Graziella Uziel24
- Valério Carelli21
- Stefano DiDonato15
- Federica Invernizzi14
- Giacomo P. Comi14
- Isabella Moroni14
- Holger Prokisch13
- Maria Lucia Valentino13
- Maurizio Moggio13
- Salvatore DiMauro13
- Serenella Servidei13
- Tobias B. Haack13
- Enrico Bertini12
- Franco Carrara12
- Raffaele Cerutti12
- Thomas Meitinger11
- Tim M. Strom11
- António Toscano10
全論文
- Mitochondrial diseases
著者: Gráinne S. Gorman, Patrick F. Chinnery, Salvatore DiMauro, Michio Hirano, Yasutoshi Koga, Robert McFarland, Anu Suomalainen, David R. Thorburn, Massimo Zeviani, Douglass M. Turnbull - Nature Reviews Disease Primers 2016 被引用: 1,534
- Identification and characterization of a spinal muscular atrophy-determining gene
著者: Suzie Lefebvre, Lydie Bürglen, Sophie Reboullet, Olivier Clermont, Philippe Burlet, Louis Viollet, Bernard Bénichou, Corinne Cruaud, Philippe Millasseau, Massimo Zeviani, Denis Le Paslier, J Frézal, Daniel Cohen, Jean Weissenbach, Arnold Münnich, Judith Melki - Cell 1995 被引用: 4,025
- Neural stem cells traffic functional mitochondria via extracellular vesicles
著者: Luca Peruzzotti‐Jametti, Joshua D. Bernstock, Cory M. Willis, Giulia Manferrari, Rebecca Rogall, Erika Fernández‐Vizarra, James C. Williamson, Alice Braga, Aletta M.R. van den Bosch, Tommaso Leonardi, Grzegorz Krzak, Ágnes Kittel, Cristiane Benincá, Nunzio Vicario, Sisareuth Tan, Carlos A. P. Bastos, Iacopo Bicci, Nunzio Iraci, Jayden A. Smith, Ben Peacock, Karin H. Müller, Paul J. Lehner, Edit I. Buzás, Nuno Faria, Massimo Zeviani, Christian Frezza, Alain Brisson, Nicholas J. Matheson, Carlo Viscomi, Stefano Pluchino - PLoS Biology 2021 被引用: 251
- Mitochondrial disorders of the OXPHOS system
著者: Erika Fernández‐Vizarra, Massimo Zeviani - FEBS Letters 2020 被引用: 309
- Mitochondrial Structure and Bioenergetics in Normal and Disease Conditions
著者: Margherita Protasoni, Massimo Zeviani - International Journal of Molecular Sciences 2021 被引用: 206
- The Opa1-Dependent Mitochondrial Cristae Remodeling Pathway Controls Atrophic, Apoptotic, and Ischemic Tissue Damage
著者: Tatiana Varanita, María Eugenia Soriano, Vanina Romanello, Tania Zaglia, Rubén Quintana–Cabrera, Martina Semenzato, Roberta Menabò, Veronica Costa, Gabriele Civiletto, Paola Pesce, Carlo Viscomi, Massimo Zeviani, Fabio Di Lisa, Marco Mongillo, Marco Sandri, Luca Scorrano - Cell Metabolism 2015 被引用: 455
- Genome editing in mitochondria corrects a pathogenic mtDNA mutation in vivo
著者: Payam A. Gammage, Carlo Viscomi, Marie‐Lune Simard, Ana S.H. Costa, Edoardo Gaude, Christopher A. Powell, Lindsey Van Haute, Beverly J. McCann, Pedro Rebelo‐Guiomar, Raffaele Cerutti, Lei Zhang, Edward J. Rebar, Massimo Zeviani, Christian Frezza, James B. Stewart, Michal Minczuk - Nature Medicine 2018 被引用: 305
- Transcription Factor EB Controls Metabolic Flexibility during Exercise
著者: Gelsomina Mansueto, Andrea Armani, Carlo Viscomi, Luca D’Orsi, Rossella De Cegli, Elena V. Polishchuk, Costanza Lamperti, Ivano Di Meo, Vanina Romanello, Silvia Marchet, Pradip Saha, Haihong Zong, Bert Blaauw, Francesca Solagna, Caterina Tezze, Paolo Grumati, Paolo Bonaldo, Jeffrey E. Pessin, Massimo Zeviani, Marco Sandri, Andrea Ballabio - Cell Metabolism 2016 被引用: 328
- Loss of function of the mitochondrial peptidase PITRM1 induces proteotoxic stress and Alzheimer’s disease-like pathology in human cerebral organoids
著者: Maria Jose Perez J., Dina Ivanyuk, Vasiliki Panagiotakopoulou, Gabriele Di Napoli, Stefanie Kalb, Dario Brunetti, Rawaa Al‐Shaana, Stephan A. Kaeser, Sabine Anne‐Kristin Fraschka, Mathias Jucker, Massimo Zeviani, Carlo Viscomi, Michela Deleidi - Molecular Psychiatry 2020 被引用: 140
- Oxygen sensing requires mitochondrial ROS but not oxidative phosphorylation
著者: Joslyn K. Brunelle, Eric L. Bell, N.M. Quesada, Kristel Vercauteren, Valeria Tiranti, Massimo Zeviani, Richard C. Scarpulla, Navdeep S. Chandel - Cell Metabolism 2005 被引用: 758
- FGF21 is a biomarker for mitochondrial translation and mtDNA maintenance disorders
著者: Jenni M. Lehtonen, Saara Forsström, Emanuela Bottani, Carlo Viscomi, Olivier R. Baris, Helena Isoniemi, Krister Höckerstedt, Pia Österlund, Mikko Hurme, Juulia Jylhävä, Sirpa Leppä, Ritva Markkula, Tiina Heliö, Giuliana Mombelli, Johanna Uusimaa, Reijo Laaksonen, Hannu Laaksovirta, Mari Auranen, Massimo Zeviani, Jan Smeıtınk, Rudolf J. Wiesner, Kazuto Nakada, Pirjo Isohanni, Anu Suomalainen - Neurology 2016 被引用: 220
- Two independent respiratory chains adapt OXPHOS performance to glycolytic switch
著者: Erika Fernández‐Vizarra, Sandra López-Calcerrada, Ana Sierra‐Magro, Rafael Pérez‐Pérez, Luke E. Formosa, Daniella H. Hock, M. E. Banegas Illescas, Ana Peñas, Michele Brischigliaro, Shujing Ding, Ian M. Fearnley, Charalampos Tzoulis, Robert D. S. Pitceathly, Joaquı́n Arenas, Miguel A. Martı́n, David A. Stroud, Massimo Zeviani, Michael T. Ryan, Cristina Ugalde - Cell Metabolism 2022 被引用: 92
- In Vivo Correction of COX Deficiency by Activation of the AMPK/PGC-1α Axis
著者: Carlo Viscomi, Emanuela Bottani, Gabriele Civiletto, Raffaele Cerutti, Maurizio Moggio, Gigliola Fagiolari, Eric A. Schon, Costanza Lamperti, Massimo Zeviani - Cell Metabolism 2011 被引用: 289
- NAD+-Dependent Activation of Sirt1 Corrects the Phenotype in a Mouse Model of Mitochondrial Disease
著者: Raffaele Cerutti, Eija Pirinen, Costanza Lamperti, Silvia Marchet, Anthony A. Sauve, Wei Li, Valerio Leoni, Eric A. Schon, Françoise Dantzer, Johan Auwerx, Carlo Viscomi, Massimo Zeviani - Cell Metabolism 2014 被引用: 345
- Neuronal complex I deficiency occurs throughout the Parkinson’s disease brain, but is not associated with neurodegeneration or mitochondrial DNA damage
著者: Irene H. Flønes, Erika Fernández‐Vizarra, Maria Lykouri, Brage Brakedal, Geir Skeie, Hrvoje Miletić, Peer K. Lilleng, Guido Alves, Ole‐Bjørn Tysnes, Kristoffer Haugarvoll, Christian Dölle, Massimo Zeviani, Charalampos Tzoulis - Acta Neuropathologica 2017 被引用: 133
- Cytochrome c oxidase deficiency
著者: Michele Brischigliaro, Massimo Zeviani - Biochimica et Biophysica Acta (BBA) - Bioenergetics 2020 被引用: 110
- Loss of ETHE1, a mitochondrial dioxygenase, causes fatal sulfide toxicity in ethylmalonic encephalopathy
著者: Valeria Tiranti, Carlo Viscomi, Tatjana M. Hildebrandt, Ivano Di Meo, Rossana Mineri, Cecilia Tiveron, Michael D. Levitt, A. Prelle, Gigliola Fagiolari, Marco Rimoldi, Massimo Zeviani - Nature Medicine 2009 被引用: 409
- Pharmacological Inhibition of Poly(ADP-Ribose) Polymerases Improves Fitness and Mitochondrial Function in Skeletal Muscle
著者: Eija Pirinen, Carles Cantó, Young Suk Jo, Laia Morató, Hongbo Zhang, Keir J. Menzies, Evan G. Williams, Laurent Mouchiroud, Norman Moullan, Carolina E. Hagberg, Wei Li, Silvie Timmers, Ralph Imhof, Jef Verbeek, Aurora Pujol, Barbara van Loon, Carlo Viscomi, Massimo Zeviani, Patrick Schrauwen, Anthony A. Sauve, Kristina Schoonjans, Johan Auwerx - Cell Metabolism 2014 被引用: 253
- Multi-system neurological disease is common in patients with OPA1 mutations
著者: Patrick Yu‐Wai‐Man, Philip G. Griffiths, Gráinne S. Gorman, Charles Marques Lourenço, Alan F. Wright, Michaela Auer‐Grumbach, António Toscano, O. Musumeci, Maria Lucia Valentino, Leonardo Caporali, Costanza Lamperti, Chantal Tallaksen, Philip Duffey, James Miller, Roger G. Whittaker, Mark R. Baker, Margaret Jackson, Michael W. Clarke, Baljean Dhillon, Birgit Czermin, Joanna D. Stewart, Gavin Hudson, Pascal Reynier, Dominique Bonneau, Wilson Marques, Guy Lenaers, Robert McFarland, Robert W. Taylor, Douglass M. Turnbull, Marcela Votruba, Massimo Zeviani, Valério Carelli, Laurence A. Bindoff, Rita Horváth, Patrizia Amati‐Bonneau, Patrick F. Chinnery - Brain 2010 被引用: 447
- A SIRT7-Dependent Acetylation Switch of GABPβ1 Controls Mitochondrial Function
著者: Dongryeol Ryu, Young Suk Jo, Giuseppe Lo Sasso, Sokrates Stein, Hongbo Zhang, Alessia Perino, Jung Uee Lee, Massimo Zeviani, R. Romand, Michael O. Hottiger, Kristina Schoonjans, Johan Auwerx - Cell Metabolism 2014 被引用: 254
- Human mitochondrial DNA deletions associated with mutations in the gene encoding Twinkle, a phage T7 gene 4-like protein localized in mitochondria
著者: Johannes N. Spelbrink, Fang-Yuan Li, Valeria Tiranti, Kaisu Nikali, Qiu-Ping Yuan, Muhammed Tariq, Sjoerd Wanrooij, Nuria Garrido, Giacomo P. Comi, Lucía Morandi, Lucio Santoro, António Toscano, Gian-Maria Fabrizi, Hannu Somer, R Croxen, David Beeson, Joanna Poulton, Anu Suomalainen, Howard T. Jacobs, Massimo Zeviani, Catharina Larsson - Nature Genetics 2001 被引用: 882
- Respiratory supercomplexes act as a platform for complex III‐mediated maturation of human mitochondrial complexes I and IV
著者: Margherita Protasoni, Rafael Pérez‐Pérez, Teresa Lobo‐Jarne, Michael E. Harbour, Shujing Ding, Ana Peñas, Francisca Díaz, Carlos T. Moraes, Ian M. Fearnley, Massimo Zeviani, Cristina Ugalde, Erika Fernández‐Vizarra - The EMBO Journal 2020 被引用: 157
- Mitochondrial Retinopathies
著者: Massimo Zeviani, Valério Carelli - International Journal of Molecular Sciences 2021 被引用: 80
- Increased longevity and refractoriness to Ca2+-dependent neurodegeneration in Surf1 knockout mice
著者: Carlotta Dell’Agnello, Laura S. Leo, A. Agostino, György Szabadkai, Cecilia Tiveron, Alessandra Zulian, A. Prelle, Pierre L. Roubertoux, Rosario Rizzuto, Massimo Zeviani - Human Molecular Genetics 2007 被引用: 310
