Kevin Talbot
Active 1995–2025
- 151
- Papers
- 20,498
- Citations
- 87
- h-index
- 138
- i10-index
Citations
Citation sources
Countries
Institutions
Fields
- Medicine66%
- Biochemistry, Genetics and Molecular Biology21.8%
- Neuroscience9.4%
- Immunology and Microbiology0.6%
- Computer Science0.4%
- Engineering0.3%
- Other1.5%
Topics
- Amyotrophic Lateral Sclerosis Research15.6%
- Neurogenetic and Muscular Disorders Research10.3%
- Parkinson's Disease Mechanisms and Treatments5.8%
- Genetic Neurodegenerative Diseases4.1%
- Alzheimer's disease research and treatments3.2%
- RNA Research and Splicing3%
- Other58%
Coauthors
- Martin R. Turner65
- Alexander G. Thompson22
- Elizabeth Gray17
- Ruxandra Dafinca15
- Ammar Al‐Chalabi14
- Jakub Scaber14
- Olaf Ansorge13
- Thomas H. Gillingwater11
- Richard Wade‐Martins9
- Christopher McDermott8
- David F. Gordon8
- Matthew C. Kiernan8
- Matthew J. A. Wood8
- Pamela J. Shaw8
- Thanuja Dharmadasa8
- Emily Feneberg7
- James N. Sleigh7
- Ricarda Menke7
- Sally A. Cowley7
- Ana Candalija6
- Andrea Malaspina6
- Björn F. Vahsen6
- Carolyn Young6
- Kay E. Davies6
All papers
- A proposal for new diagnostic criteria for ALS
Authors: Jeremy M. Shefner, Ammar Al‐Chalabi, Mark R. Baker, Liying Cui, Mamede de Carvalho, Andrew Eisen, Julian Großkreutz, Orla Hardiman, Robert D. Henderson, José Manuel Matamala, Hiroshi Mitsumoto, Walter J. Paulus, Neil G. Simon, Michael Swash, Kevin Talbot, Martin R. Turner, Yoshikazu Ugawa, Leonard H. van den Berg, Renato J. Verdugo, S. Vucic, Ryuji Kaji, David Burke, Matthew C. Kiernan - Clinical Neurophysiology 2020 cited by 574
- Extracellular vesicles in neurodegenerative disease — pathogenesis to biomarkers
Authors: Alexander G. Thompson, Elizabeth Gray, Sabrina M. Heman-Ackah, Imre Mäger, Kevin Talbot, Samir EL Andaloussi, Matthew J. A. Wood, Martin R. Turner - Nature Reviews Neurology 2016 cited by 424
- Neurofilament light chain
Authors: Ching‐Hua Lu, Corrie Macdonald‐Wallis, Elizabeth Gray, Neil Pearce, Axel Petzold, Niklas Norgren, Gavin Giovannoni, Pietro Fratta, Katie Sidle, Mark Fish, Richard W. Orrell, Robin Howard, Kevin Talbot, Linda Greensmith, Jens Kühle, Martin R. Turner, Andrea Malaspina - Neurology 2015 cited by 551
- Truncated stathmin-2 is a marker of TDP-43 pathology in frontotemporal dementia
Authors: Mercedes Prudencio, Jack Humphrey, Sarah Pickles, Anna‐Leigh Brown, Sarah E. Hill, Jennifer M. Kachergus, Jianhua Shi, Michael G. Heckman, Matthew R. Spiegel, Casey Cook, Yuping Song, Mei Yue, Lillian M. Daughrity, Yari Carlomagno, Karen Jansen‐West, Cristhoper Fernandez De Castro, Michael DeTure, Shunsuke Koga, Ying‐Chih Wang, Prasanth Sivakumar, Cristian Bodo, Ana Candalija, Kevin Talbot, Bhuvaneish T. Selvaraj, Karen Burr, Siddharthan Chandran, Jia Newcombe, Tammaryn Lashley, Isabel Hubbard, Demetra Catalano, Duyang Kim, Nadia Propp, Samantha Fennessey, Delphine Fagegaltier, Hemali Phatnani, Maria Secrier, Elizabeth Fisher, Björn Oskarsson, Marka van Blitterswijk, Rosa Rademakers, N. R. Graff-Radford, Bradley F. Boeve, David S. Knopman, Ronald C. Petersen, Keith A. Josephs, E. Aubrey Thompson, Towfique Raj, Michael E. Ward, Dennis W. Dickson, Tania F. Gendron, Pietro Fratta, Leonard Petrucelli - Journal of Clinical Investigation 2020 cited by 257
- Frequency of the C9orf72 hexanucleotide repeat expansion in patients with amyotrophic lateral sclerosis and frontotemporal dementia: a cross-sectional study
Authors: Elisa Majounie, Alan E. Renton, Kin Y. Mok, Elise G.P. Dopper, Adrian J. Waite, Sara Rollinson, Adriano Chiò, Gabriella Restagno, Nayia Nicolaou, Javier Simón‐Sánchez, John C. van Swieten, Yevgeniya Abramzon, Janel O. Johnson, Michael Sendtner, Roger Pamphlett, Richard W. Orrell, Simon Mead, Katie Sidle, Henry Houlden, Jonathan D. Rohrer, Karen Morrison, Hardev Pall, Kevin Talbot, Olaf Ansorge, Dena G. Hernandez, Sampath Arepalli, Mario Sabatelli, Gabriele Mora, Massimo Corbo, Fabio Giannini, Andrea Calvo, Elisabet Englund, Giuseppe Borghero, Gianluca Floris, Anne M. Remes, Hannu Laaksovirta, Leo McCluskey, John Q. Trojanowski, Vivianna M. Van Deerlin, Gerard D. Schellenberg, Michael A. Nalls, Vivian E. Drory, Chin‐Song Lu, Tu‐Hsueh Yeh, Hiroyuki Ishiura, Yuji Takahashi, Shoji Tsuji, Isabelle Le Ber, Alexis Brice, Carsten Drepper, Nigel Williams, Janine Kirby, Pamela J. Shaw, John Hardy, Pentti J. Tienari, Peter Heutink, Huw R. Morris, Stuart Pickering‐Brown, Bryan J. Traynor - The Lancet Neurology 2012 cited by 1,226
- Prognosis for patients with amyotrophic lateral sclerosis: development and validation of a personalised prediction model
Authors: Henk-Jan Westeneng, Thomas P. A. Debray, Anne E Visser, Ruben P. A. van Eijk, James Rooney, Andrea Calvo, Sarah Martin, Christopher McDermott, Alexander G. Thompson, Susana Pinto, Xenia Kobeleva, Angela Rosenbohm, Beatrice Stubendorff, Helma Sommer, Bas Middelkoop, Annelot M. Dekker, Joke J.F.A. van Vugt, Wouter van Rheenen, Alice Vajda, Mark Heverin, Mbombe Kazoka, Hannah Hollinger, Marta Gromicho, Sonja Körner, Thomas Ringer, Annekathrin Rödiger, A. Gunkel, Christopher E. Shaw, Annelien L. Bredenoord, Michael A. van Es, Philippe Corcia, Philippe Couratier, Markus Weber, Julian Großkreutz, Albert C. Ludolph, Susanne Petri, Mamede de Carvalho, Philip Van Damme, Kevin Talbot, Martin R. Turner, Pamela J. Shaw, Ammar Al‐Chalabi, Adriano Chiò, Orla Hardiman, Karel G.M. Moons, Jan H. Veldink, Leonard H. van den Berg - The Lancet Neurology 2018 cited by 517
- Improving clinical trial outcomes in amyotrophic lateral sclerosis
Authors: Matthew C. Kiernan, Steve Vucic, Kevin Talbot, Christopher McDermott, Orla Hardiman, Jeremy M. Shefner, Ammar Al‐Chalabi, William Huynh, Merit Cudkowicz, Paul Talman, Leonard H. van den Berg, Thanuja Dharmadasa, Paul Wicks, C.M. Reilly, Martin R. Turner - Nature Reviews Neurology 2020 cited by 291
- Axonal TDP-43 condensates drive neuromuscular junction disruption through inhibition of local synthesis of nuclear encoded mitochondrial proteins
Authors: Topaz Altman, Ariel Ionescu, Amjad Ibraheem, Dominik Priesmann, Tal Gradus-Pery, Luba Farberov, Gayster Alexandra, Natalia Shelestovich, Ruxandra Dafinca, Noam Shomron, Florence Rage, Kevin Talbot, Michael E. Ward, Amir Dori, Marcus Krüger, Eran Perlson - Nature Communications 2021 cited by 139
- ER Stress and Autophagic Perturbations Lead to Elevated Extracellular α-Synuclein in GBA-N370S Parkinson's iPSC-Derived Dopamine Neurons
Authors: Hugo J. R. Fernandes, Elizabeth M. Hartfield, Helen Christian, Evangelia Emmanoulidou, Ying Zheng, Heather Booth, Helle Bogetofte, Charmaine Lang, Brent J. Ryan, S. Pablo Sardi, Jennifer L. Badger, Jane Vowles, Samuel Evetts, George K. Tofaris, Kostas Vekrellis, Kevin Talbot, Michele T. Hu, William James, Sally A. Cowley, Richard Wade‐Martins - Stem Cell Reports 2016 cited by 365
- Multicentre appraisal of amyotrophic lateral sclerosis biofluid biomarkers shows primacy of blood neurofilament light chain
Authors: Alexander G. Thompson, Elizabeth Gray, Nick Verber, Yoana Bobeva, Vittoria Lombardi, Stephanie Shepheard, Özlem Yildiz, Emily Feneberg, Lucy Farrimond, Thanuja Dharmadasa, Pamela Gray, Evan Edmond, Jakub Scaber, Delia Gagliardi, Janine Kirby, Thomas M. Jenkins, Pietro Fratta, Christopher McDermott, Sanjay Manohar, Kevin Talbot, Andrea Malaspina, Pamela J. Shaw, Martin R. Turner - Brain Communications 2022 cited by 81
- Non-neuronal cells in amyotrophic lateral sclerosis — from pathogenesis to biomarkers
Authors: Björn F. Vahsen, Elizabeth Gray, Alexander G. Thompson, Olaf Ansorge, Daniel C. Anthony, Sally A. Cowley, Kevin Talbot, Martin R. Turner - Nature Reviews Neurology 2021 cited by 147
- Impairment of Mitochondrial Calcium Buffering Links Mutations in C9ORF72 and TARDBP in iPS-Derived Motor Neurons from Patients with ALS/FTD
Authors: Ruxandra Dafinca, Paola Barbagallo, Lucy Farrimond, Ana Candalija, Jakub Scaber, Nidaa A. Ababneh, Chaitra Sathyaprakash, Jane Vowles, Sally A. Cowley, Kevin Talbot - Stem Cell Reports 2020 cited by 131
- NEK1 variants confer susceptibility to amyotrophic lateral sclerosis
Authors: Kevin P. Kenna, Perry T.C. van Doormaal, Annelot M. Dekker, Nicola Ticozzi, Brendan Kenna, Frank P. Diekstra, Wouter van Rheenen, Kristel R. van Eijk, Ashley R Jones, Pamela Keagle, Aleksey Shatunov, William Sproviero, Bradley Smith, Michael A. van Es, Simon Topp, Aoife Kenna, Jack W. Miller, Claudia Fallini, Cinzia Tiloca, Russell L. McLaughlin, Caroline Vance, Claire Troakes, Claudia Colombrita, Gabriele Mora, Andrea Calvo, Federico Verde, Safa Al‐Sarraj, Andrew King, Daniela Calini, Jacqueline de Belleroche, Frank Baas, Anneke J. van der Kooi, Marianne de Visser, Anneloor L.M.A. ten Asbroek, Peter C. Sapp, Diane McKenna‐Yasek, Meraida Polak, Seneshaw Asress, José Luís Muñoz-Blanco, Tim M. Strom, Thomas Meitinger, Karen Morrison, Giuseppe Lauria, Kelly L. Williams, P. Nigel Leigh, Garth A. Nicholson, Ian P. Blair, Claire S. Leblond, Patrick A. Dion, Guy A. Rouleau, Hardev Pall, Pamela J. Shaw, Martin R. Turner, Kevin Talbot, Franco Taroni, Khrista Boylan, Marka van Blitterswijk, Rosa Rademakers, Jesús Esteban‐Pérez, Alberto García‐Redondo, Phillip Van Damme, Wim Robberecht, Adriano Chiò, Cinzia Gellera, Carsten Drepper, Michael Sendtner, Antonia Ratti, Jonathan D. Glass, Jesús S. Mora, Nazlı Başak, Orla Hardiman, Albert C. Ludolph, Peter M. Andersen, Jochen H. Weishaupt, Robert H. Brown, Ammar Al‐Chalabi, Vincenzo Silani, Christopher E. Shaw, Leonard H. van den Berg, Jan H. Veldink, John E. Landers - Nature Genetics 2016 cited by 294
- C9orf72-ALS human iPSC microglia are pro-inflammatory and toxic to co-cultured motor neurons via MMP9
Authors: Björn F. Vahsen, Sumedha Nalluru, Georgia R. Morgan, Lucy Farrimond, Emily Carroll, Yinyan Xu, Kaitlyn M. L. Cramb, Benazir Amein, Jakub Scaber, Antigoni Katsikoudi, Ana Candalija, Mireia Carcolé, Ruxandra Dafinca, Adrian M. Isaacs, Richard Wade‐Martins, Elizabeth Gray, Martin R. Turner, Sally A. Cowley, Kevin Talbot - Nature Communications 2023 cited by 72
- Mutations in the vesicular trafficking protein annexin A11 are associated with amyotrophic lateral sclerosis
Authors: Bradley Smith, Simon Topp, Claudia Fallini, Hideki Shibata, Han-Jou Chen, Claire Troakes, Andrew King, Nicola Ticozzi, Kevin P. Kenna, Athina Soragia-Gkazi, Jack W. Miller, Akane Sato, Diana Marques Dias, Maryangel Jeon, Caroline Vance, Chun Hao Wong, Martina de Majo, Wejdan Kattuah, Jacqueline C. Mitchell, Emma L. Scotter, Nicholas Parkin, Peter C. Sapp, Matthew Nolan, Peter J. Nestor, Michael A. Simpson, Michael E. Weale, Monkel Lek, Frank Baas, J. M. Vianney de Jong, Anneloor L.M.A. ten Asbroek, Alberto García‐Redondo, Jesús Esteban‐Pérez, Cinzia Tiloca, Federico Verde, Stefano Duga, Nigel Leigh, Hardev Pall, Karen Morrison, Ammar Al‐Chalabi, Pamela J. Shaw, Janine Kirby, Martin R. Turner, Kevin Talbot, Orla Hardiman, Jonathan D. Glass, Jacqueline de Belleroche, Masatoshi Maki, Stephen E. Moss, Christopher C.J. Miller, Cinzia Gellera, Antonia Ratti, Safa Al‐Sarraj, Robert H. Brown, Vincenzo Silani, John E. Landers, Christopher E. Shaw - Science Translational Medicine 2017 cited by 247
- The influence of age and gender on motor and non-motor features of early Parkinson's disease: Initial findings from the Oxford Parkinson Disease Center (OPDC) discovery cohort
Authors: Konrad Szewczyk‐Królikowski, Paul Tomlinson, Kannan Nithi, Richard Wade‐Martins, Kevin Talbot, Yoav Ben‐Shlomo, Michele T.M. Hu - Parkinsonism & Related Disorders 2013 cited by 302
- The clinical landscape for SMA in a new therapeutic era
Authors: Kevin Talbot, Eduardo F. Tizzano - Gene Therapy 2017 cited by 174
- Exome-wide Rare Variant Analysis Identifies TUBA4A Mutations Associated with Familial ALS
Authors: Bradley Smith, Nicola Ticozzi, Claudia Fallini, Soragia Athina Gkazi, Simon Topp, Kevin P. Kenna, Emma L. Scotter, Jason Kost, Pamela Keagle, Jack W. Miller, Daniela Calini, Caroline Vance, Eric Danielson, Claire Troakes, Cinzia Tiloca, Safa Al‐Sarraj, Elizabeth Lewis, Andrew King, Claudia Colombrita, Viviana Pensato, Barbara Castellotti, Jacqueline de Belleroche, Frank Baas, Anneloor L.M.A. ten Asbroek, Peter C. Sapp, Diane McKenna‐Yasek, Russell L. McLaughlin, Meraida Polak, Seneshaw Asress, Jesús Esteban‐Pérez, José Luís Muñoz-Blanco, Michael A. Simpson, Wouter van Rheenen, Frank P. Diekstra, Giuseppe Lauria, Stefano Duga, Stefania Corti, Cristina Cereda, Lucia Corrado, Gianni Sorarú, Karen Morrison, Kelly L. Williams, Garth A. Nicholson, Ian P. Blair, Patrick A. Dion, Claire S. Leblond, Guy A. Rouleau, Orla Hardiman, Jan H. Veldink, Leonard H. van den Berg, Ammar Al‐Chalabi, Hardev Pall, Pamela J. Shaw, Martin R. Turner, Kevin Talbot, Franco Taroni, Alberto García‐Redondo, Zheyang Wu, Jonathan D. Glass, Cinzia Gellera, Antonia Ratti, Robert H. Brown, Vincenzo Silani, Christopher E. Shaw, John E. Landers, Sandra D’Alfonso, Letizia Mazzini, Giacomo P. Comi, Roberto Del Bo, Mauro Ceroni, Stella Gagliardi, Giorgia Querin, Cinzia Bertolin - Neuron 2014 cited by 370
- C9orf72 Hexanucleotide Expansions Are Associated with Altered Endoplasmic Reticulum Calcium Homeostasis and Stress Granule Formation in Induced Pluripotent Stem Cell-Derived Neurons from Patients with Amyotrophic Lateral Sclerosis and Frontotemporal Dementia
Authors: Ruxandra Dafinca, Jakub Scaber, Nidaa A. Ababneh, Tatjana Lalic, Greg A. Weir, Helen Christian, Jane Vowles, Andrew G. L. Douglas, Alexandra Fletcher-Jones, Cathy Browne, Mahito Nakanishi, Martin R. Turner, Richard Wade‐Martins, Sally A. Cowley, Kevin Talbot - Stem Cells 2016 cited by 244
- Correction of amyotrophic lateral sclerosis related phenotypes in induced pluripotent stem cell-derived motor neurons carrying a hexanucleotide expansion mutation in C9orf72 by CRISPR/Cas9 genome editing using homology-directed repair
Authors: Nidaa A. Ababneh, Jakub Scaber, Rowan Flynn, Andrew G. L. Douglas, Paola Barbagallo, Ana Candalija, Martin R. Turner, David Sims, Ruxandra Dafinca, Sally A. Cowley, Kevin Talbot - Human Molecular Genetics 2020 cited by 76
- CSF extracellular vesicle proteomics demonstrates altered protein homeostasis in amyotrophic lateral sclerosis
Authors: Alexander G. Thompson, Elizabeth Gray, Imre Mäger, Marie‐Laëtitia Thézénas, Philip D. Charles, Kevin Talbot, Román Fischer, Benedikt M. Kessler, Matthew J. A. Wood, Martin R. Turner - Clinical Proteomics 2020 cited by 60
- Targeting phosphoglycerate kinase 1 with terazosin improves motor neuron phenotypes in multiple models of amyotrophic lateral sclerosis
Authors: Helena Chaytow, Emily Carroll, David F. Gordon, Yu-Ting Huang, Dinja van der Hoorn, Hannah Smith, Thomas Becker, Catherina G. Becker, Kiterie M. E. Faller, Kevin Talbot, Thomas H. Gillingwater - EBioMedicine 2022 cited by 56
- HDAC6 is a therapeutic target in mutant GARS-induced Charcot-Marie-Tooth disease
Authors: Veronick Benoy, Lawrence Van Helleputte, Robert Prior, Constantin d’Ydewalle, Wanda Haeck, Natasja Geens, Wendy Scheveneels, Begga Schevenels, M. Zameel Cader, Kevin Talbot, Alan P. Kozikowski, Pieter Vanden Berghe, Philip Van Damme, Wim Robberecht, Ludo Van Den Bosch - Brain 2017 cited by 122
- The impact of age on genetic testing decisions in amyotrophic lateral sclerosis
Authors: Puja R. Mehta, Alfredo Iacoangeli, Sarah Opie-Martin, Joke J.F.A. van Vugt, Ahmad Al Khleifat, Andrea Bredin, Lynn Ossher, Peter M. Andersen, Orla Hardiman, Arpan R. Mehta, Pietro Fratta, Kevin Talbot, Nazlı Başak, Philippe Corcia, Philippe Couratier, Mamede de Carvalho, Vivian E. Drory, Jonathan D. Glass, Marc Gotkine, John E. Landers, Russell L. McLaughlin, Jesús S. Mora Pardina, Karen Morrison, Mónica Povedano, Christopher E. Shaw, Pamela J. Shaw, Vincenzo Silani, Nicola Ticozzi, Philip Van Damme, Leonard H. van den Berg, Jan H. Veldink, Patrick Vourc’h, Markus Weber, Ammar Al‐Chalabi - Brain 2022 cited by 48
